Cochlear Implantation in Children with Inner Ear Malformation and Cochlear Nerve Deficiency

Kimitaka Kaga, M.D., Ph.D.Emeritus Director, National Institute of Sensory Organs, National Tokyo Medical Center

“The book is directed at otologists or pediatric otolaryngologists with an interest in cochlear implantation as well as audiologists treating these patients. … This is an excellent primer for surgeons and audiologists interested in inner ear malformations and their treatment. This is a highly technical topic, and the book is most suitable for otologists/pediatric otolaryngologists or researchers with an interest in this area.” (Jacob Eide, Doody's Book Reviews, October 25, 2019)

• 1. Overview.- Part I. Basic Researches.- 2. Embryology of inner ear and its malformation.- 3. Embryology of cochlear and vestibular nerve and its deficiency.- 4. Morphology and molecular biology of spiral ganglion.- 5. Genetics of inner ear malformation and cochlear nerve deficiency.- Part II. Clinical Researches.- 6. New classification of inner ear malformations and cochlear nerve deficiency by temporal bone imaging.- 7. Outcome of inner ear malformations and auditory neuropathy spectrum disorders after cochlear implantation in children.- 8. EABR of inner ear malformation and cochlear nerve deficiency after cochlear implantation in children.- 9. Vestibular neuropathy.- 10. Vestibular development in children with inner ear malformation and cochlear nerve deficiency.- 11. Vestibular myogenic potential after cochlear implant.- 12. Speech and hearing in children with inner ear malformation and cochlear nerve deficiency.