Peter Wurnig – författare

With improvements in respirator therapy and intensive care, congenital malformations and various acquired pathologic deformities of the trachea or bronchi are more often observed than used to be the case. For a while it seemed that tracheostomy would be unnecessary, but it has since become quite clear that severe disturbance of the trachea would be the outcome owing to primary or secondary pathologic changes that had not been given adequate consideration previous. These changes can lead to urgent life-threatening episodes or definite mutilation for the rest of the child''s life. Tracheal surgery thus repre­ sents a new and special challenge for the pediatric surgeon. A solution to these serious problems must be found and merits discussion. Further­ more, it seems worthwhile to review cases of surgical pulmonary dis­ eases, except for the already widely discussed problems ofempyemas or bronchiectasis. P. WURNIG, Vienna Contents Pathophysiology of Subglottic Tracheal Stenosis in Childhood. B.MINNIGERODE and H.G.RICHTER. With2Figures 1 Subglottic Stenosis in Newborns After Mechanical Ventilation. M.MARCOVICH, F.POLLAUF, and K.BURIAN. With 3 Figures ... 8 Treatment of Congenital Cricoid Stenosis. R.N. P. BERKOVITS, E.J. VAN DER SCHANS, and J. C. MOLENAAR. With 7 Figures . . .. 20 Surgical Correction of Laryngotracheal Stenoses in Children. E. HOF. With 6 Figures . . . . . . . . . . . . . . . . . . . . .. 29 Surgical Treatment of Congenital Laryngotracheo-oesophageal Cleft. R.N.P.BERKOVITS, N.M.A.BAX, and E.J. VAN DER SCHANS.

With improvements in respirator therapy and intensive care, congenital malformations and various acquired pathologic deformities of the trachea or bronchi are more often observed than used to be the case. For a while it seemed that tracheostomy would be unnecessary, but it has since become quite clear that severe disturbance of the trachea would be the outcome owing to primary or secondary pathologic changes that had not been given adequate consideration previous. These changes can lead to urgent life-threatening episodes or definite mutilation for the rest of the child's life. Tracheal surgery thus repre­ sents a new and special challenge for the pediatric surgeon. A solution to these serious problems must be found and merits discussion. Further­ more, it seems worthwhile to review cases of surgical pulmonary dis­ eases, except for the already widely discussed problems ofempyemas or bronchiectasis. P. WURNIG, Vienna Contents Pathophysiology of Subglottic Tracheal Stenosis in Childhood. B.MINNIGERODE and H.G.RICHTER. With2Figures 1 Subglottic Stenosis in Newborns After Mechanical Ventilation. M.MARCOVICH, F.POLLAUF, and K.BURIAN. With 3 Figures ... 8 Treatment of Congenital Cricoid Stenosis. R.N. P. BERKOVITS, E.J. VAN DER SCHANS, and J. C. MOLENAAR. With 7 Figures . . .. 20 Surgical Correction of Laryngotracheal Stenoses in Children. E. HOF. With 6 Figures . . . . . . . . . . . . . . . . . . . . .. 29 Surgical Treatment of Congenital Laryngotracheo-oesophageal Cleft. R.N.P.BERKOVITS, N.M.A.BAX, and E.J. VAN DER SCHANS.

Wir berichten tiber 185 Kinder mit unterschiedlichen Erscheinungen, die her- kommlich als Riesenhamartom, Angiodysplasie, kongenitale Trophoedem, ort- licher Gigantismus (z. B. Macrodaktylie) usw. gekennzeichnet werden. Wir schla- gen vor, aIle diese Erscheinungen als eine Entitat zu verstehen: kongenitale Weich- teildysplasie (congenital soft-tissue dysplasia, CSTD. Nach jtingsten embryologischen und zellbiologischen Untersuchungen tritt die CSTD als Folge embryonaler oder fetaler biosynthetischer Zellfehlregulation auf. Das Konzept einer CSTD-Entitat fiihrt sowohl zu einem gemeinsamen Unter- suchungsprotokoll als auch zu einem gemeinsamen therapeutischen Vorgehen un- ter besonderer Berticksichtigung der "Stabilitat" und der Gutartigkeit des Zu- standes. Die Behandlung sollte auf die funktionelle Verbesserung beschrankt bleiben, anstatt die Korrektur kosmetischer Defekte zu versuchen. References 1. Andre JM (1973) Les dysplasies vasculaires systematisees, vol 1. L'expansion scientifique, Paris 2. Andre JM, Jacquier A, Picard L (1977) La neurofibromatose de Recklinghausen. Pathogenie - Conception actuelle. Ann Chir Thor Cardiovasc 16: 175-185 3.Andrews EJ, Ward BC, Altman NH (1979) Spontaneous animal models of human diseases, vols 1 and 2. Academic, New York 4. Azouz EM (1983) Hematuria, rectal-bleeding and pelvic phleboliths in children with Klippel- Trenaunay syndrome. Pediatr Radiol 13: 82-88 5. Barksy AJ (1967) Macrodactyly. J Bone Joint Surg 49A(7): 1255-1266 6. Berliner DL, Ruhmann AG (1966) Comparison of growth of fibroblasts under the influence of II-beta-hydroxy and ll-keto-corticosteroids. Endocrinology 78: 373 7. Chassaignac C (1959) Hypertrophie congenitale des 2 membres droits. Bull Soc Coo Paris 8.